КЛИНИЧЕСКИЙ СЛУЧАЙ СИНДРОМА «СЛИВОВОГО ЖИВОТА», ПОТРЕБОВАВШИЙ ТРАНСПЛАНТАЦИИ ПОЧКИ В ДЕТСКОМ ВОЗРАСТЕ

И.В. Горемыкин; Ю.М. Спиваковский; Е.И. Краснова; Н.А. Кузнецова

doi:10.56871/UTJ.2023.26.62.013

CLINICAL CASE OF PRUNE BELLY SYNDROME REQUIRING KIDNEY TRANSPLANT IN CHILDHOOD

I.V. Goremykin Saratov State Medical University named after V.I. Razumovsky. Bol’shaya Kazach’ya st., 112, Saratov, Russian Federation, 410012
Yu.M. Spivakovskiy Saratov State Medical University named after V.I. Razumovsky. Bol’shaya Kazach’ya st., 112, Saratov, Russian Federation, 410012
E.I. Krasnova Saratov State Medical University named after V.I. Razumovsky. Bol’shaya Kazach’ya st., 112, Saratov, Russian Federation, 410012
N.A. Kuznetsova Saratov State Medical University named after V.I. Razumovsky. Bol’shaya Kazach’ya st., 112, Saratov, Russian Federation, 410012

Keywords:

синдром «сливового живота» клинический случай дети мегацистис врожденные пороки развития мочевыделительной системы хроническая болезнь почек трансплантация почки катамнез prune belly syndrome clinical case children megacystis congenital malformations of the urinary tract chronic kidney disease kidney transplant catamnesis

Abstract

Background. Prune belly syndrome is a multisystem disease that is clinically manifested by a combination of hypoplasia of the abdominal muscles, bilateral cryptorchidism, and congenital anomalies of the urinary system of varying severity. The article provides insight in etiopathogenesis, criteria for differentiating patients according to the severity of manifestations, based on description of the clinical case. Case presentation. Prune belly syndrome was diagnosed at the first examination of the boy at the age of 7 months. Staged surgical treatment of bilateral refluxing ureterohydronephrosis, orchiopexy at the age of 1 to 3 years was carried out. However, the loss of kidney function progressed, the patient underwent a kidney transplant from his mother at the age of 11 years. The follow-up of this patient to the age of 15 years was presented and evaluation of the results of surgical treatment was provided. Conclusion. The prognosis for the life and health of patients with prune belly syndrome is mainly determined by the degree of renal parenchyma dysplasia. An multidisciplinary approach involving urologists, nephrologists, surgeons, endocrinologists and other specialists allows us to improve urodynamics, to achieve stable remission of chronic obstructive pyelonephritis to perform kidney transplant in childhood with a good result.

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Goremykin, I., Spivakovskiy, Y., Krasnova, E., & Kuznetsova, N. (2023). CLINICAL CASE OF PRUNE BELLY SYNDROME REQUIRING KIDNEY TRANSPLANT IN CHILDHOOD. University Therapeutic Journal, 5(3), 128-136. https://doi.org/10.56871/UTJ.2023.26.62.013

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